Submitted by linda on Sat, 12/07/2019 - 12:16

The complexity of HHD can be compounded by superimposed eczema herpeticum (EH) or Kaposi's varicelliform eruption, which is caused by a viral infection occurring in preexistent cutaneous conditions. We present a unique clinical presentation of HHD with superimposed EH caused by herpes simplex virus type 2 (HSV-2) infection managed in a burn unit. It is highly advised that a recalcitrant HHD with superimposed EH caused by HSV-2 infection should be managed in burn centers that offer multimodalities for prompt, rigorous management. Early diagnosis and treatment are highly suggested for EH to avoid fatal complications.

Copyright © 2019, Chin et al.

 

Chin AGM1Asif M2Hultman C3Caffrey J2.

Author information

1 General Surgery, St. John's Episcopal Hospital, Far Rockaway, USA.

2 Surgery, Burn Center, The Johns Hopkins University School of Medicine, Baltimore, USA.

3 Plastic Surgery, The Johns Hopkins University School of Medicine, Baltimore, USA.

PMID: 31777694

PMCID: PMC6853267

DOI: 10.7759/cureus.5907

Free PMC Article

Abstract

Familial benign pemphigus, or Hailey-Hailey disease (HHD), is a rare (1 in 50,000), benign, autosomal dominant cutaneous disorder that causes a painful rash and blistering commonly occurring in the intertriginous folds. Despite having a good prognosis, there is no cure for HHD and the disease can be quite debilitating to the quality of life.